Table 2

Patients with Rare Causes of Spine Deformity. Note that cases such Noonan syndrome and scoliosis related to extraspinal congenital anomalies don't fit to SRS classification

Underlying Disorder
N

II. Neuromuscular (paralytic)

a) Neurologic disorder

- progressive hemidystonia
1
- Rett syndrome
1
b) Muscular disorder

- facioscapulohumeral muscular dystrophy
1
- arthrogryposis
1

V. Mesenchymal disorders

- Marfan syndrome
1

IX. Osteochondrodystrophies

- Spondyloepiphyseal dysplasia congenita
1

XI. Metabolic disorders

- Osteogenesis imperfecta
2
- Osteopetrosis tarda (Albers-Schonberg disease)
1
- Cleidocranial dysplasia
1

Other

Noonan syndrome
1
Related to other congenital disorders

- Phocomelia
1
- Congenital blindness
1

Total
13

Soultanis et al. Scoliosis 2007 2:15   doi:10.1186/1748-7161-2-15